Use Additional code(s) to identify organ or system involvement, such as encephalitis (G05.3)

Code first Revised to poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4)

Code first alkaptonuria (E70.29)

ochronosis (E70.29)

Excludes2: postprocedural scoliosis (M96.89)

postradiation scoliosis (M96.5)

Code first neoplasm (C49.-, C79.89, D21.-, D48.1-)

Disorders of bone density and structure (M80-M85)

Excludes1: vitamin D-resistant osteomalacia (E83.31)

vitamin D-resistant rickets (active) (E83.31)

Other osteopathies (M86-M90)

Code first osteolysis (M89.5-)

Code first vitamin-D-resistant rickets (E83.31)

Periprosthetic fracture around internal prosthetic joint (M97)

Code first, if known, the specific type and cause of fracture, such as traumatic or pathological

Excludes2: ostium primum atrial septal defect (type I) (Q21.20)

Other congenital malformations of the digestive system (Q38-Q45)

Code also, if applicable, associated malformations affecting other systems

Add Congenital malformation of liver, NOS

Accessory liver

Congenital absence of liver

Congenital hepatomegaly

Congenital malformations and deformations of the musculoskeletal system (Q65-Q79)

Excludes1: sagittal craniosynostosis (Q75.01)

Excludes1: coronal craniosynostosis (Q75.02-)

lambdoid craniosynostosis (Q75.04-)

Craniosynostosis NOS

Non-deformational dolichocephaly

Non-deformational scaphocephaly

Excludes1: plagiocephaly (Q67.3)

Non-deformational anterior plagiocephaly

Excludes1: dolichocephaly (Q67.2)

Non-deformational anterior plagiocephaly

Non-deformational brachycephaly

Trigonocephaly

Non-deformational posterior plagiocephaly

Excludes1: dolichocephaly (Q67.2)

Excludes1: coronal craniosynostosis, bilateral (Q75.022)

lambdoid craniosynostosis, bilateral (Q75.042)

Other congenital malformations (Q80-Q89)

Excludes1:  Revise to Menkes’ kinky hair syndrome (E83.09)

Asadollahi-Rauch syndrome

Mediator complex subunit 13L syndrome

Code also, if applicable, any associated manifestations such as:

• autism spectrum disorder
• (F84.0-)congenital malformations of cardiac septa (Q21-)
• epilepsy and recurrent seizures (G40.-)
• intellectual disability (F70-F79)

Chromosomal abnormalities, not elsewhere classified (Q90-Q99)

Code also associated physical condition(s), such as atrioventricular septal defect(Q21.2-)

Use Additional code(s) to identify any associated degree of intellectual disabilities (F70-F79)

22q13.3 deletion syndrome

Use Additional code(s) to identify any associated conditions, such as:

• autism spectrum disorder (F84.0)
• degree of intellectual disabilities (F70-F79)
• epilepsy and recurrent seizures (G40.-)
• lymphedema (I89.0)

Encounter for child welfare screening exam

Excludes2: encounter for examination and observation for alleged child physical abuse (Z04.72)

encounter for examination and observation for alleged child rape (Z04.42)

Encounter for observation of newborn for apnea alarm without findings

Encounter for observation of newborn for bradycardia alarm without findings

Encounter for observation of newborn for malfunction of home cardiorespiratory monitor

Encounter for observation of newborn for non-specific findings home physiologic monitoring device

Encounter for observation of newborn for pulse oximeter alarm without findings

Excludes1: encounter for observation for suspected conditions related to home physiologic monitoring device ruled out (Z03.83)

neonatal bradycardia (P29.12)

other newborn apnea (P28.4-)

primary sleep apnea of newborn (P28.3-)